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타깃 · 모달리티 · 임상 근거 · 비임상 맥락으로 최대 5개 프로그램을 나란히 비교합니다. · 다음 갱신 D-6 · 마지막 9월 2일

현재 선택: 2

프로그램 상세에서 관심 등록 후 2개 이상 모으면 여기서 한 번에 비교할 수 있습니다.

API CSV27행 · 2개 프로그램

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항목
CGTCurated CoreFDAApproved
etranacogene dezaparvovec (Hemgenix, AMT-061, CSL222, etranacogene dezaparvovec-drlb)
CSL Behring·Factor IX (AAV5 Padua)
7 trials
CGTCurated CoreFDAApproved
valoctocogene roxaparvovec (Roctavian, BMN 270, valoctocogene roxaparvovec-rvox)
BioMarin·Factor VIII (AAV5)
8 trials
Overview
Program
Hemgenix (etranacogene dezaparvovec)Roctavian (valoctocogene roxaparvovec)
Overview
Company
CSL BehringBioMarin
Overview
Modality
CGTCGT
Overview
Target
Factor IX (AAV5 Padua)Factor VIII (AAV5)
Overview
Indication
Hemophilia B (congenital Factor IX deficiency) in adultsSevere hemophilia A in adults
Overview
Phase
APPROVEDAPPROVED
Overview
Status
APPROVEDAPPROVED
Overview
Content status
Curated CoreCurated Core
Overview
Data Confidence
Data Confidence · HighData Confidence · High
Overview
Development Signal
Development Signal · EstablishedDevelopment Signal · Established
Overview
Approval status
FDA approvedFDA approved
Positioning
Key differentiator
High-activity FIX Padua enables durable FIX levels from liver-directed AAV5First FDA-approved gene therapy for hemophilia A
Positioning
Known limitation
ALT elevations, infusion reactions; AAV5 NAb screeningbypassing agents (BPAs), recombinant factor VIII (rFVIII), recombinant factor VIII Fc fusion protein (rFVIIIFc), and gene ther
Positioning
Development positioning
First FDA-approved gene therapy for hemophilia BGene therapy alternative to Emicizumab / FVIII prophylaxis
Technology
Vector
AAV5AAV5
MoA
Mechanism
Etranacogene dezaparvovec (AAV5) delivers FIX Padua transgene to hepatocytes for sustained Factor IX expression in hemophilia B.Valoctocogene roxaparvovec (AAV5-hFVIII) provides liver-directed Factor VIII expression for severe hemophilia A.
MoA
Biomarker
FIX activity (IU/dL), annualized bleeding rate.FVIII activity, ABR.
PK/PD
Species
NHP, Mouse, FIX activity post-infusion, ABR reductionCynomolgus monkey
PK/PD
Animal (cat.)
Human, Mouse, NHPNHP
PK/PD
Experiment
pharmacokineticbiodistribution
PK/PD
Biodistribution
Hepatotropic AAV5 IV infusion
Toxicology
Species
NHP, MouseCynomolgus monkey
Toxicology
Major finding
Transient hepatotoxicity / ALT rise; corticosteroid managementHepatocellular enzyme elevations; steroid protocols
Clinical
Safety signal
Transient hepatotoxicity / ALT rise; corticosteroid managementHepatocellular enzyme elevations; steroid protocols
Clinical
Program phase
APPROVEDAPPROVED
Clinical
Trial activity
4 recruiting · 2 completed1 recruiting · 6 completed
Preclinical
Animal (cat.)
NHP